Rosai-Dorfman disease of the lung with features of obliterative arteritis

Jose G. Mantilla, Anna Shmukler, Yanhua Wang

Research output: Contribution to journalArticlepeer-review

1 Scopus citations


Sinus histiocytosis with massive lymphadenopathy, also known as Rosai-Dorfman disease (RDD), is a rare benign non-Langerhans cell histiocytosis. Twenty-five to forty percent of the cases are extranodal and have been reported in virtually all anatomic locations. In this article, we report a highly unusual case of RDD which presented as multiple pulmonary nodules and associated hilar lymphadenopathy. On resection, extensive obliterative arteritis was noticed. This pathologic presentation of RDD has not been reported before in the English literature. Accurate recognition of this entity is crucial to prevent unnecessary aggressive treatment.

Original languageEnglish (US)
Pages (from-to)135-138
Number of pages4
JournalJournal of Hematopathology
Issue number3
StatePublished - Sep 1 2016


  • Lung
  • Obliterative arteritis
  • Rosai-Dorfman disease

ASJC Scopus subject areas

  • Pathology and Forensic Medicine
  • Histology
  • Hematology


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