Congenital soft tissue stenosis of the external auditory canal with canal cholesteatoma: Case report and literature review

Alanna M. Windsor; Ryan Ruiz; Robert C. O'Reilly

doi:10.1016/j.ijporl.2020.110053

Congenital soft tissue stenosis of the external auditory canal with canal cholesteatoma: Case report and literature review

Alanna M. Windsor, Ryan Ruiz, Robert C. O'Reilly

Research output: Contribution to journal › Article › peer-review

1 Scopus citations

Abstract

Congenital external auditory canal stenosis (EACS) is a spectrum of abnormalities affecting the external and middle ear. We report a 6 year-old patient with EACS affecting the lateral fibrocartilaginous canal that was successfully repaired. This patient highlights a variant of EACS characterized by lateral soft tissue narrowing with normal osseous development. Most previous studies of CAA have described severe forms associated with complete atresia, bony stenosis, and middle ear malformations. Stenosis affecting only the fibrocartilaginous canal is a milder form resulting from premature arrest of the canalization process during embryologic development, and may predispose to cholesteatoma formation.

Original language	English (US)
Article number	110053
Journal	International journal of pediatric otorhinolaryngology
Volume	134
DOIs	https://doi.org/10.1016/j.ijporl.2020.110053
State	Published - Jul 2020
Externally published	Yes

Keywords

Cholesteatoma
Conductive
External auditory canal stenosis
Hearing loss
Pediatric otology

ASJC Scopus subject areas

Pediatrics, Perinatology, and Child Health
Otorhinolaryngology

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10.1016/j.ijporl.2020.110053

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title = "Congenital soft tissue stenosis of the external auditory canal with canal cholesteatoma: Case report and literature review",

abstract = "Congenital external auditory canal stenosis (EACS) is a spectrum of abnormalities affecting the external and middle ear. We report a 6 year-old patient with EACS affecting the lateral fibrocartilaginous canal that was successfully repaired. This patient highlights a variant of EACS characterized by lateral soft tissue narrowing with normal osseous development. Most previous studies of CAA have described severe forms associated with complete atresia, bony stenosis, and middle ear malformations. Stenosis affecting only the fibrocartilaginous canal is a milder form resulting from premature arrest of the canalization process during embryologic development, and may predispose to cholesteatoma formation.",

keywords = "Cholesteatoma, Conductive, External auditory canal stenosis, Hearing loss, Pediatric otology",

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year = "2020",

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language = "English (US)",

volume = "134",

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T2 - Case report and literature review

AU - Windsor, Alanna M.

AU - Ruiz, Ryan

AU - O'Reilly, Robert C.

PY - 2020/7

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N2 - Congenital external auditory canal stenosis (EACS) is a spectrum of abnormalities affecting the external and middle ear. We report a 6 year-old patient with EACS affecting the lateral fibrocartilaginous canal that was successfully repaired. This patient highlights a variant of EACS characterized by lateral soft tissue narrowing with normal osseous development. Most previous studies of CAA have described severe forms associated with complete atresia, bony stenosis, and middle ear malformations. Stenosis affecting only the fibrocartilaginous canal is a milder form resulting from premature arrest of the canalization process during embryologic development, and may predispose to cholesteatoma formation.

AB - Congenital external auditory canal stenosis (EACS) is a spectrum of abnormalities affecting the external and middle ear. We report a 6 year-old patient with EACS affecting the lateral fibrocartilaginous canal that was successfully repaired. This patient highlights a variant of EACS characterized by lateral soft tissue narrowing with normal osseous development. Most previous studies of CAA have described severe forms associated with complete atresia, bony stenosis, and middle ear malformations. Stenosis affecting only the fibrocartilaginous canal is a milder form resulting from premature arrest of the canalization process during embryologic development, and may predispose to cholesteatoma formation.

KW - Cholesteatoma

KW - Conductive

KW - External auditory canal stenosis

KW - Hearing loss

KW - Pediatric otology

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Congenital soft tissue stenosis of the external auditory canal with canal cholesteatoma: Case report and literature review

Abstract

Keywords

ASJC Scopus subject areas

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