Myelodysplastic syndrome presenting as a Behçet's-like disease with aortitis

Shudan Wang, Noam Broder, Paula Marchetta, Johannes Nowatzky

Research output: Contribution to journalArticlepeer-review

3 Scopus citations


A 46-year-old Hispanic man presented with fever, genital ulcers, left eye redness and chest pain. Physical examination was notable for a healed oral ulcer and scrotal ulcers, and bilateral superficial thrombophlebitis. He was found to have new-onset pancytopenia. CT of the chest showed pericardial and pleural effusions and rapidly progressing inflammation of the aortic arch and ascending vessels. Although the patient had Behcet's disease (BD)-like symptoms, pancytopenia could not be explained by the diagnosis, prompting a bone marrow biopsy which showed myelodysplastic syndrome. This report highlights the importance of excluding alternate disorders before making a diagnosis of Behcet's disease if atypical, BD-incompatible or incomplete constellations of symptoms and findings are present.

Original languageEnglish (US)
Article number220649
JournalBMJ case reports
StatePublished - 2018
Externally publishedYes


  • haematology (incl blood transfusion)
  • rheumatology
  • vasculitis

ASJC Scopus subject areas

  • Medicine(all)


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