Linear segmental neurofibromatosis in an L5 distribution

Background and Objective: Neurofibromatosis (NF) is a neurocutaneous disorder with seven subtypes;segmental NF-1 is characterized by neurofibromas and or café-au-lait macules in one or more dermatomes, primarily the thorax and abdomen. We present the rare case of a 36-year-old African-American female with isolated, multiple soft nodules in a linear configuration on the plantar and dorsal surfaces of the left foot. Conclusion: This is the first report of isolated segmental NF-1 in a unique linear pattern confined to the L5 dermatome.